RE:
UROGENITAL INVOLVEMENT IN THE KLIPPEL-TRENAUNAY-WEBER SYNDROME. TREATMENT
OPTIONS AND RESULTS FABIO C. VICENTINI, FRANCISCO T. DENES, CRISTIANO M. GOMES, ALEXANDRE DANILOVIC, FREDERICO A. SILVA, MIGUEL SROUGI Division of Urology, University of Sao Paulo School of Medicine (USP), Sao Paulo, Brazil Int Braz J Urol, 32: 697-704, 2006
With
the intention to provide more information about this rare and difficult
disease, we communicate that the boy from the Case 3 underwent a right
transfemoral amputation due to massive enlargement and walking inability
in November 2006. In January 2007, he had a massive enterorrhagia probably
related to the growth of the vascular tumor and involvement of the colon.
Despite multiple transfusions and medical measures, stabilization was
not achieved and he died before surgical procedure could be attempted.
The patient of the Case 1 is a mulatto man, and not a black man as described. Dr.
Fabio C. Vicentini |